Late Involution Of Obstructive Rhabdomyoma Of The Mitral Valve

Abstract

This study is not associated with any post-graduation program.A male patient had presented signs of mitral valve obstruction since birth (fatigue during nursing, left atrial enlargement, diastolic gradient = 7 mmHg), which then regressed since 9 months of age. Masses identified at the mitral valve echocardiogram, right ventricular septum and left anterior papillary muscle led to a diagnosis of rhabdomyoma. Currently 14 years of age, the patient performs normal physical and mental activities. A late involution of the mitral valve mass was observed, partial at 5 years and total at 14 years of age. The mass measured 15x14mm up to 28 months of age, 14x11mm at 5 years and 12x10mm at 8 years of age. The other masses, which were non-obstructive, decreased. The expectant management showed a peculiar late involution of the rhabdomyoma.