Punch-out Lesion Following Regression Of A Large Left Ventricular Outflow Rhabdomyoma
Abu Zahira, I. A., & Nir, A. (2018). Punch-out lesion following regression of a large left ventricular outflow rhabdomyoma. Cardiology in the young, 28(1), 153–154. https://doi.org/10.1017/S1047951117001512
View Original Source →Abstract
s We report the case of a patient with rhabdomyoma of the left ventricular outflow tract, causing severe obstruction at birth. The tumour regressed completely by 6 years of age, leaving a punch-out lesion. The potential for spontaneous regression of these tumours and the formation of a myocardial lesion following rhabdomyoma regression are discussed.
Case Details
Disease Location
Heart
Personal Characteristics
8-year-old boy
Clinical Characteristics
Patient diagnosed with tuberous sclerosis WHO was born with multiple cardiac rhabdomyomas. At birth, the echocardiogram revealed a large lobulated hyperechogenic mass within the intraventricular septum extending into the left ventricular outflow tract and causing severe flow obstruction
Remission Characteristics
At 6 years of age the tumour in the left ventricular outflow tract had completely disappeared, leaving a punch-out lesion. The other tumours also disappeared, and were replaced by myocardium
Treatment & Mechanisms
Proposed Remission Mechanisms
None reported
Non-Clinical Treatment
None reported