Spontaneous Closure Of Muscular Ventricular Septal Defect By Growth Of Right Ventricular Muscle Bundles: A Rare Mechanism
Charaf Eddine, A., Kadiu, G., & Sanil, Y. (2020). Spontaneous closure of muscular ventricular septal defect by growth of right ventricular muscle bundles: a rare mechanism. Cardiology in the young, 30(2), 291–293. https://doi.org/10.1017/S1047951119002920
View Original Source →Abstract
We present a case of an 18-year-old male with large anterior muscular ventricular septal defect. Assessment by echocardiography showed that the defect has completely closed by the growth of muscle bundles that formed a pouch-like structure on the right ventricular side. This unusual mechanism of closure has been reported in one prior case report. In our report, we present images obtained by three-dimensional echocardiography.
Case Details
Disease Location
Heart
Personal Characteristics
18-year-old bengali male, history is significant for development delay with severe cognitive impairment, pectus excavatum, and scoliosis.
Clinical Characteristics
Referred to paediatric cardiology clinic for evaluation because of history of cardiac septal defect. Parents reported that patient was diagnosed with a large cardiac septal defect in early infancy. Echocardiogram showed a large muscular ventricular septal defect. Color flow doppler showed bi-directional flow across the defect.
Remission Characteristics
Transoesophageal echocardiogram was performed to further assess his cardiac anatomy. It confirmed the presence of a large anterior muscular ventricular septal defect. Color doppler interrogation of the defect showed bidirectional flow. Muscle bundles on the right ventricular side of the defect formed a pouch-like structure that totally covered the defect. There was no evidence of interventricular shunt
Treatment & Mechanisms
Proposed Remission Mechanisms
Growth of muscle bundles on the right ventricular side.