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[cardiac Tumors With Neonatal Disclosure. Apropos Of A Case With Spontaneously Favorable Development]

Isnard-Baladi et al., 1985Other/Unknown

Isnard-Baladi, J., Iselin, M., Venezia, R., Potier, J. C., & Foucault, J. P. (1985). Tumeurs cardiaques à révélation néonatale. A propos d'un cas d'évolution spotaneousanément favorable [Cardiac tumors with neonatal disclosure. Apropos of a case with spontaneously favorable development]. Archives des maladies du coeur et des vaisseaux, 78(5), 785–789.

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Abstract

The authors report the case of a cardiac tumour documented by 2 D echocardiography, presenting in the newborn with cardiac arrest. The echocardiographic features of multiple nodules disseminated in the ventricular walls suggested a diagnosis of rhabdomyoma. The initial course was complicated by poorly tolerated attacks of tachycardia which were rapidly brought under control with amiodarone. The long term outcome was clinically favourable with a rapid regression of the number and size of the tumours on echocardiography, and a tendency to normalisation of the electrocardiogramme. The possibility of regression, which has already been reported by many investigators, suggests that these cardiac tumours may have a better prognosis than previously thought.

Case Details

Disease Location

Left ventricle, apex, right & left surfaces of intraventricular septum

Personal Characteristics

Male newborn

Clinical Characteristics

Admitted at age 8 days with cardiac failure chest radiography showed massive cardiomegaly with heart to chest ratio of 0.7 & normal pulmonary vascularization echocardiogram revealed dense, homogenous images--> echogenicity higher than surrounding myocardium

Remission Characteristics

At age 5 mths, clinical exam normal heart volume regressed considerably echogenic masses (decreased in size & normal) found in contact with lateral wall of left ventricle, apex at 11 mths, tachycardia recurred but ecg did not change & amiodarone was increased at 16 mths, tachycardia did not recur echocardiography revealed small echogenic masses, pericardium free, ventricular contractility normal--> amiodarone treatment cancelled

Treatment & Mechanisms

Clinical Treatment

Treated with digitalis & diuretics when high frequency tachycardia appeared administered amiodarone & clinical condition improved