Benign Mesenchymal Tumor Of The Heart. Spontaneous Regression And Disappearance Of Pulmonary Artery Stenosis
Lee, Y. C., Singleton, R. T., & Tang, C. K. (1982). Benign mesenchymal tumor of the heart. spontaneous regression and disappearance of pulmonary artery stenosis. Chest, 82(4), 503–505. https://doi.org/10.1378/chest.82.4.503
View Original Source →Case Details
Disease Location
Right side of heart
Personal Characteristics
20- months-old male
Clinical Characteristics
Since age of 14 days, he had been admitted due to several instances of dyspnea & wheezing found to have marked cardiomegaly & failed treatment of digitalis blood pressure 100/60 mmhg with frequent premature beats heart enlarged (grade 3/6 ejection systolic murmur heard over base & 2nd heart sound at pulmonic area widely split) electrocardiogram revealed sinus tachycardia with frequent ventricular premature beats & right bundle branch block chest x-ray film revealed marked cardiomegaly & large mass lesion on right side of heart at base angiocardiogram revealed large tissue mass on anterior right side of heart & compression of right pulmonary artery biopsy specimen consisted of fragments 0.8 x 1.2 cm in aggregate tumor composed of spindle cells entirely
Remission Characteristics
In ensuing postoperative years, dyspnea & wheezing improved gradually blood pressure, pulse rate normal heart not enlarged, no murmur heard chest x-ray film showed no evidence of cardiomegaly & pleuropericardial scarring on right mediastinal area present cardiac catheterization revealed no evidence of intracardiac shunts follow-up chest x-rays revealed no cardiomegaly, ecg unchanged & echocardiogram normal
Treatment & Mechanisms
Clinical Treatment
Right heart catheterization performed & revealed no evidence of intracardiac shunt exploratory thoracotomy performed year later--> large, multinodular mass arising from right ventricular wall extending to pulomary artery