Regression Of A Coronary Arterial Fistula In An Infant With Pulmonary Atresia And An Intact Ventricular Septum
Popoiu, A., Eicken, A., Genz, T., Schreiber, C., & Hess, J. (2010). Regression of a coronary arterial fistula in an infant with pulmonary atresia and an intact ventricular septum. Pediatric cardiology, 31(1), 144–146. https://doi.org/10.1007/s00246-009-9559-2
View Original Source →Abstract
This report describes a premature newborn with pulmonary atresia and an intact ventricular septum who presented with a significant fistula between the right ventricle and the left anterior descending coronary artery (LAD). The right ventricle was not decompressed to prevent myocardial damage. After 2 months, the fistula had closed spontaneously. The pulmonary valve was opened, and biventricular circulation was achieved.
Case Details
Disease Location
Heart
Personal Characteristics
Premature newborn boy (34 weeks gestation, 2.2 kg) with cyanosis and respiratory distress.
Clinical Characteristics
Significant fistula between the right ventricle and the left anterior descending coronary artery.
Remission Characteristics
After 2 months of last clinical visit, the fistula closed spontaneously. The pulmonary valve was opened and biventricular circulation was achieved.
Treatment & Mechanisms
Proposed Remission Mechanisms
Later decompression of the right ventricle followed by a biventricular circulation
Clinical Treatment
Prostaglandin e2. Balloon atrial septemberostomy. Systemic to-pulmonary arterial shunt and atrioseptemberotomy. Ductus closed surgically.