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Spontaneous Healing Of Langerhans Cell Histiocytosis (histiocytosis-x)

Corbeel et al., 1988Other/Unknown

European Journal of Pediatrics 148(1): Oct 1988; 32-33

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Case Details

Personal Characteristics

A 3-month-old male infant, d. B., without past history

Clinical Characteristics

Presented with pallor, hepatomegaly (4.5 centimeters), splenomegaly (1.5 centimeters), anaemia (hb 6 gm/dl) and thrombocytopenia (16 x 109/l). Liver biopsy showed histiocytic infiltration. Hepatomegaly diminished after 6 months and a second liver biopsy showed decreased histiocytic infiltration. After 14 months, the hepatomegaly had disappeared completely and there were no more abnormal haematological or clinical findings.

Remission Characteristics

Hepatomegaly diminished after 6 months and disappeared completely after 14 months. No more abnormal haematological or clinical findings after 14 months.

Treatment & Mechanisms

Proposed Remission Mechanisms

Not discussed

Clinical Treatment

No treatment was given.

Additional Notes

The patient’s lymphocytes, co-cultured with neonatal lymphocytes, were positive for virus-like particles without reverse transcriptase activity. A second viral blood culture remained negative.